Abstract

BORDINO, Lucas et al. Melkersson Rosenthal syndrome: Report of two pediatric cases. Arch. argent. pediatr. [online]. 2016, vol.114, n.4, pp.e224-e227. ISSN 0325-0075.  http://dx.doi.org/10.5546/aap.2016.e224.

Melkersson Rosenthal syndrome is a very infrequent disease of unknown etiology, chronic and progressive course, with neurocutaneous disease that affects the orofacial innervation and mucocutaneous tissues with non-caseating granulomatous infiltration. Clinically, it is characterized by the diagnostic triad: recurrent edema of lips and/or face; recurrent and alternating acute peripheral facial paralysis and scrotal or geographic tongue. The condition generally presents as oligosymptomatic or monosymptomatic form. Two patients are presented with completed triad and oligosymptomatic form. This recent review published by G. Kayabasoglu et al. states that only 30 patients have been described in the international literature in childhood. So we consider this disease in the differential diagnosis in the presence of acute peripheral facial paralysis and/or lips or facial edema.

Keywords : Melkersson-Rosenthal syndrome; Facial paralysis; Recurrence; Geographic tongue.

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