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Archivos argentinos de pediatría
versión impresa ISSN 0325-0075versión On-line ISSN 1668-3501
Resumen
ALVAREZ, Pilar et al. Acrodermatitis enteropathica. Arch. argent. pediatr. [online]. 2007, vol.105, n.6, pp.536-538. ISSN 0325-0075.
Acrodermatitis enteropathica is a rare autosomal recesive disorder, caused by impaired absorption of zinc dietary intake. It is characterized by a triad of alopecia, diarrhea and acral and periorificial dermatitis. We report an 11 month-old girl with tipical symptoms in whom the diagnosis was confirmed by decreased plasma zinc level (37,7 µg%). The patient was given zinc sulfate 5 mg/kg/day and showed marked improvement.
Palabras clave : Acrodermatitis enteropathica; Zinc.