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Revista argentina de dermatología

versión On-line ISSN 1851-300X

Resumen

LORENZO, R Serra; RUIZ, G Mínguez  y  VEGA, CM Sanz. REVIEW OF THE LITERATURE ON PRIMARY EXTRAMAMMARY PAGET DISEASE IN SCROTUM: A PURPOSE OF A CASE. Rev. argent. dermatol. [online]. 2018, vol.99, n.4, pp.43-50. ISSN 1851-300X.

Extramammary Paget disease is an intraephithelial adenocarcinoma very rare. Its diagnosis is usually late and may take up to 3 years. We must make a differential diagnosis with other dermatological diseases that can occur equally. The definitive diagnosis is histopatological. Surgery is the gold standard treatment, Mohs micrographic surgery being the most used. There are topical treatments such as imiquimod that may be useful. In general, the prognosis is usually favorable.

Palabras clave : extramammary Paget disease; adenocarcinoma; Mohs surgery..

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