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Archivos argentinos de pediatría

versão impressa ISSN 0325-0075versão On-line ISSN 1668-3501

Resumo

PALMIERI, Florencia et al. Diencephalic syndrome in a child with chronic malnutrition and hyperactivity. Arch. argent. pediatr. [online]. 2018, vol.116, n.5, pp.e667-e670. ISSN 0325-0075.  http://dx.doi.org/10.5546/aap.2018.e667.

Diencephalic syndrome is an infrequent cause of malnutrition. It is produced by a malfunctioning hypothalamus, and it is related to encephalic tumors. Patients present a serious and progressive weight loss although the appetite and calorie intake are, usually, adequate. Neurological symptoms typically have a late appearance, delaying diagnostic suspicion. We present a patient aged 2 years and a half with grade II chronic malnutrition, referred with presumptive diagnosis of celiac disease, with poor adherence and treatment failure. During hospitalization, diagnosis of diencephalic syndrome secondary to grade I pilocytic astrocytoma was reached.

Palavras-chave : Malnutrition; Diencephalic syndrome; Pilocytic astrocytoma.

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