SciELO - Scientific Electronic Library Online

vol.67 número5Cáncer experimental e inflamación sistémica en un modelo murinoSíndrome de Frey por submaxilectomía y tratamiento con toxina botulínica índice de autoresíndice de materiabúsqueda de artículos
Home Pagelista alfabética de revistas  

Servicios Personalizados




  • No hay articulos citadosCitado por SciELO

Links relacionados

  • No hay articulos similaresSimilares en SciELO


Medicina (Buenos Aires)

versión impresa ISSN 0025-7680versión On-line ISSN 1669-9106


HERRERA, Ramón N. et al. Pheochromocytoma associated with von Recklinghausen neurofibromatosis. Medicina (B. Aires) [online]. 2007, vol.67, n.5, pp.475-477. ISSN 0025-7680.

A pheochromo cytoma is an adrenal gland tumor that secretes epinephrine and norepinephrine hormones, and is responsible for regulating heart rate and blood pressure, among other functions. The condition can occur alone or in combination with other disorders, and genetic and environmental factors play a key role. Neurofibromatosis- 1 (NF-1) an inherited "autosomal dominant" disorder is one of the most common genetic disorders, characterized by formation of neurofibromas (tumors involving nerve tissue) in the skin, subcutaneous tissue, cranial and spinal root nerves. NF1 generally is diagnosed by physical examination. There is no cure for NF1, but there are ways to treat some of its effects. Neurofibromatosis arterial hypertension caused by pheochromocytoma is extremely rare, less frecuent than 1% in childrens less than 10 years old, and young adults. We present a case of an extremely infrequent association between neurofibromatosis and a pheochromocytoma in a young woman with a newly diagnosed hypertension. We discuss the underlying pathophysiological mechanisms and clinical implications.

Palabras clave : Pheochromocytoma; Neurofibromatosis; Arterial hypertension; Treatment.

        · resumen en Español     · texto en Español     · Español ( pdf )


Creative Commons License Todo el contenido de esta revista, excepto dónde está identificado, está bajo una Licencia Creative Commons