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Archivos argentinos de pediatría
versión impresa ISSN 0325-0075versión On-line ISSN 1668-3501
Resumen
FERNANDEZ, María F. et al. Neonate with linear rows of vesiculobullous lesions. Arch. argent. pediatr. [online]. 2010, vol.108, n.1, pp.e5-e8. ISSN 0325-0075.
We report the case of an 8-days-old patient with linear rows of vesiculobullous lesions from birth. Along with these lesions, the neonate had eosinophilia, which made us arrive to the clinical diagnosis of Incontinentia Pigmenti. Incontinentia Pigmenti or Bloch Sulzberger disease is a multisystemic neuroectodermal disorder that affects mostly women, which includes as initial manifestation cutaneous lesions that evolve by outbreaks. Occasionally, it is associated with neurologic, ophthalmologic, and dental compromise. This must be considered as a differential diagnosis when a neonate presents vesiculobullous lesions.
Palabras clave : Neonate; Vesiculobullous lesions; Incontinentia Pigmenti; Bloch Sulzberger syndrome.