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Archivos argentinos de pediatría

versión impresa ISSN 0325-0075

Resumen

DEL TORO-VALERO, Azucena et al. Amniotic band sequence and bilateral choanal atresia: a case report. Arch. argent. pediatr. [online]. 2011, vol.109, n.4, pp.e77-e81. ISSN 0325-0075.

Amniotic band sequence (ABS) is a group malformation that mainly affects limbs; clinically, constriction rings and lymphedema of the fngers, arms and legs, acrosyndactyly and pseudosyndactyly are observed; also there is congenital amputation of limbs due to distal swelling. Less frequently, craniofacial and trunk involvement are reported in some patients. Etiology is still unknow and most cases are isolated. In this report we present the case of a 45-day-old male with diagnosis of SBA and bilateral choanal atresia as attached fnding, and review possible causes of SBA and associated alterations.

Palabras clave : Amniotic band sequence; Bilateral choanal atresia; Limb; Craniofacial and trunk disruption.

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