Archivos argentinos de pediatría
versão impressa ISSN 0325-0075
CONCHA R, Marcela et al. Pilomatrixoma: unusual clinical presentation. Arch. argent. pediatr. [online]. 2011, vol.109, n.6, pp. 116-118. ISSN 0325-0075. http://dx.doi.org/10.5546/aap.2011.e116.
Pilomatrixoma is a rare, benign neoplasm that is derived from hair matrix cells. It is more frequent during childhood, especially between the ages of 5 and 15 years. Pilomatrixoma is usually a hard, well circumscribed, solitary lesion, and can be located on any part of the body, except palms and soles, with a predilection for maxilofacial region. Multiple pilomatrixomas are rare and they have been associated with various systemic syndromes, of which myotonic dystrophy has been the most described. The diagnosis of pilomatrixoma is fundamentally clinical. Complementary studies such as ultrasound can be useful to confrm the diagnosis. Excisional surgery is the standard curative treatment. We present a 17-year-old female patient with an extremely uncommon clinical presentation of pilomatrixoma: multiple lesions, anetodermic, and rapid growth.
Palavras-chave : Pilomatrixoma; Benign skin tumor in children.