Abstract

OESCHGEF, Vanesa Verónica  and  PRIETO, Mariana. Mauriac syndrome in Argentina in the XXI century: series of 5 cases. Arch. argent. pediatr. [online]. 2014, vol.112, n.2, pp.e46-e49. ISSN 0325-0075.  http://dx.doi.org/10.5546/aap.2014.e46.

Mauriac syndrome is associated with poor metabolic control of type 1 diabetes mellitus, hepatomegaly and elevated transaminases characterized by growth failure and delayed puberty, which may be reversible with good glycemic control. There are few references published in recent years following the introduction of glycemic self-monitoring, new insulins and intensified treatment. We describe a series of five patients evaluated in our service with Mauriac syndrome characteristics, conducting a literature review of cases in Argentina.

Keywords : Síndrome de Mauriac; Diabetes mellitus; Hepatomegalia; Edemas.

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