Abstract

REYES-BARAONA, Francisco et al. Linear IgA bullous dermatosis of childhood: case report. Arch. argent. pediatr. [online]. 2014, vol.112, n.2, pp.e57-e60. ISSN 0325-0075.  http://dx.doi.org/10.5546/aap.2014.e57.

Linear IgA bullous dermatosis is a rare acquired autoinmune vesiculobullous disease characterized by linear IgA deposit on the dermo-epidermal basement membrane observed with direct inmunofluorescence. The characteristic lesions are vesicles and tense serous bullae, which most often are grouped giving a "cluster of jewels" appearance. Differential diagnosis must be established with other autoimmune dermatosis, such as dermatitis herpetiformis and bullous pemphigoid. Dapsone is the first line therapy, with excellent response in a short period. This is a benign disease that tends to wax and wane in severity until it disappears spontaneously. We report the case of a 5-year-old girl presenting with bullous lesions, being diagnosed a linear IgA bullous dermatosis, with excellent response to dapsone in less than 2 weeks.

Keywords : Linear IgA bullous dermatosis of childhood; Bullous diseases.

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