Abstract

ªANLIDAG, Burçin; BALKAN, Ceyhun  and  BAHCECILER, Nerin. A case report: incomplete Kawasaki disease in a hypogammaglobulinémie child. Arch. argent. pediatr. [online]. 2018, vol.116, n.2, pp.e322-e324. ISSN 0325-0075.  http://dx.doi.org/10.5546/aap.2018.e322.

Kawasaki Disease (KD) is a systemic autoimmune vasculitis that affects small and medium sized vessels. Main complication of Kawasaki Disease is coronary artery aneurism, which has higher risk in case of delayed diagnosis and treatment. Although, complete and incomplete KD cases in different types of immune deficiency diseases have been presented up to date, clinical course of KD in patients with hypogammaglobulinemia (HG) has not been reported. Herein, a case diagnosed as incomplete KD in a child with transient HG of infancy has been reported. Previously reported cases with KD and immunedeficiency have also been summarized. Recurrent infections in case of immunedeficiency may mask KD disease resulting in delay in diagnosis and increased risk of complication. KD should be kept in mind in immunedeficient patients in case of prolonged fever.

Keywords : Kawasaki disease; Hypogammaglobulinemia; Immune deficiency.