Revista argentina de cardiología
versión On-line ISSN 1850-3748
ARIAS, Aníbal et al. Cardiac Amyloidosis with Dynamic Subaortic Obstruction. Rev. argent. cardiol. [online]. 2011, vol.79, n.5, pp. 453-456. ISSN 1850-3748.
Primary amyloidosis is a systemic infiltrative disease that compromises the heart and represents an important cause of restrictive cardiomyopathy. We describe the case of a patient with heart failure secondary to an infiltrative cardiomyopathy with amyloid deposition and dynamic left ventricular outflow tract obstruction. The hematological diagnosis was light chain multiple myeloma with presence of amyloidosis in two extracardiac tissues. The echocardiogram revealed substantial wall thickening with significant dynamic subaortic obstruction; the magnetic resonance imaging showed a pattern suggestive of amyloid infiltration. An endomyocardial biopsy confirmed the diagnosis of cardiac amyloidosis. This is the first case of this atypical presentation of cardiac amyloidosis reported in our country.
Palabras llave : Amyloidosis; Cardiomyopathy; Hypertrophic; Heart Failure-diagnosis; Endomyocardial biopsy.