Abstract

OCAMPO, E; VERDI, M; BALSELLS, L  and  ZUSAETA, M. Discovering the elasticum pseudoxanthoma. Rev. argent. dermatol. [online]. 2006, vol.87, n.1, pp.6-14. ISSN 1851-300X.

Hereditary disease does not frequent pseudoxanthoma elastic; is a genetic upheaval of the conective weave, that characterizes by fragmentation of elastic fibers and later calcification of these, affecting dermis, blood vessels and membrane of Bruch of retina. The inheritance pattern is very variable which causes that disease; can be subdiagnosed. The litlle incidence of this pathology, causes that in our professional experience we have been able to diagnose two cases in which the manifestations were cutaneous.

Keywords : Pseudoxanthoma elasticum; Elastic fibers; Disease systemic; Genodermatoses.

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