Abstract

PEREZ-ELIZONDO, AD  and  FLORES MIRANDA, R. Urticaria pigmentosa: a case report of adulthood development. Rev. argent. dermatol. [online]. 2014, vol.95, n.4, pp.45-51. ISSN 1851-300X.

We report the case of a female patient of 41 years-old, with disseminated dermatosis on trunk and proximal portion of the extremities, characterized by highly itching maculopapular rash of chronic course with exacerbations, caused by external physical and thermal stimuli with partial remissions treated with oral antihistamines irregularly. The clinical diagnosis of urticaria pigmentosa was made and confirmed by pathologic examination. Urticaria pigmentosa is the most common variant of the wide spectrum of mastocytosis, a disease occasionally observed in children and rarely in adults, without internal organ involvement. The interest of this presentation is based on the low reported prevalence of this disease in adulthood without evidence of infiltrative involvement of the medullar and bone tissue in regular monitoring of control.

Keywords : Mastocytosis; Urticaria pigmentosa; Adulthood.