Abstract

MEZMEZIAN M, M et al. A low-grade myxofibrosarcoma of the chest wall. Rev. argent. dermatol. [online]. 2016, vol.97, n.3, pp.22-26. ISSN 1851-300X.

Myxofibrosarcoma is an uncommon soft tissue sarcoma that is grading as low or high malignancy. The principal sites of involvement are the lower limbs. Clinical recognition is difficult since it resembles a cyst, a lipoma, other soft tissue sarcoma or even benign conditions as panniculitis. The wide surgical excision is the main therapeutic approach because local recurrence is frequent. The high grade variant is associated in 30 % of the cases with distant metastasis, especially to the lung, bone and lymph nodes. The histopathological features allow an accurate diagnosis in most cases. A 43 year-old man with a myxofibrosarcoma of the chest wall is reported with a follow-up of two years without recurrence.

Keywords : myxofibrosarcoma; soft tissue tumors; low-grade fibromyxoid sarcoma.