Abstract

PEREZ ELIZONDO, AD  and  SANCHEZ-CASTILLO, JL. Wegener’s  granulomatosis: A pediatric case report. Rev. argent. dermatol. [online]. 2018, vol.99, n.1, pp.1-10. ISSN 1851-300X.

Wegener's granulomatosis is a necrotizing granulomatous vasculitis, that affects the upper respiratory tract, lower and glomeruli. This and microscopic polyangiitis are vascular diseases associated with neutrophil cytoplasmic antibodies (ANCA). Wegener's granulomatosis is a rare disease, cause not yet de?ned, with an incidence of 0.4 cases per 100.000 inhabitants. We report the case of a male patient of 14 years old, no medical history of importance but with C3 and C4 report normal, positive ANA and positive c-ANCA 1:40. The literature review updates the knowledge about this disease that allows the clinician to diagnose keeps it in mind to try.

Keywords : necrotizing granulomatous vasculitis; glomeruli; upper respiratory tract; neutrophil cytoplasmic antibodies (ANCA); Wegener's granulomatosis.