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Revista argentina de endocrinología y metabolismo
versión On-line ISSN 1851-3034
Resumen
ACOSTA, J.M. y HERRERA, C.N.. Systemic lupus erythematosus associated a McCune-Albright syndrome: case report. Rev. argent. endocrinol. metab. [online]. 2018, vol.55, n.3, pp.51-60. ISSN 1851-3034.
McCune-Albright Syndrome (MAS) is a rare disease characterized by a classical triad: polyostotic fibrous dysplasia (PFD), cafe-au-lait macules and endocrine abnormalities, most frequently precocious puberty. This syndrome has not been associated with autoimmune diseases. We report the first case of a patient with MAS and systemic lupus erythematosus.
Palabras clave : Systemic lupus erythematosus; Fibrous dysplasia polyostotic; McCune-Albright syndrome; Precocious puberty.