Abstract

TABAJ, Gabriela; GIUGNO, Eduardo; ROSSI, Santiago  and  VASCONCELOS, Thiago. Síndrome de Hughes-Stovin. Rev. am. med. respir. [online]. 2015, vol.15, n.3, pp.253-255. ISSN 1852-236X.

The Hughes-Stovin Syndrome (HSS) is a very rare clinical disorder characterized by thrombophlebitis and multiple pulmonary and/or bronchial aneurysms. The exact etiology and pathogenesis of HSS is unknown; possible causes include infections and angiodysplasia. HSS has also been considered as a variant of Behcet's disease (BD). Patients with HSS usually present with cough, dyspnea, fever, chest pain and haemoptysis. Early diagnosis and treatment are important, because patients are at a high risk for devastating pulmonary artery aneurysm rupture. Treatment usually involves immunosuppressive agents.

Keywords : Hughes-Stovin Syndrome; Pulmonary aneurysms.

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