Abstract

QUEIROZ DE FRANCA¹, Júlio César; FERNANDES DE GODOY², Moacir; RIBEIRO SPOTTI³, Mariane  and  DOS SANTOS4, Márcio Antonio. Insuf. card. [online]. 2018, vol.13, n.1, pp.40-44. ISSN 1852-3862.

The anomalous origin of the coronary artery from the pulmonary artery (ALCAPA or White-Bland-Garland syndrome) is a rare congenital cardiopathy. It presents predominantly in childhood and its main presentation forms are myocardial ischemia and heart failure. The survival to adulthood is unusual. If not treated, mortality by ALCAPA syndrome is close to 90% in childhood, therefore, the early recognition and surgical repair are essential. We present the case of a 56 years old woman, followed by our ambulatory with the ALCAPA Syndrome diagnosis, and recent functional class and dyspnea worsening

Keywords : Bland-White-Garland syndrome; Coronary anomalies; Coronary angiotomography.

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