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Revista argentina de reumatología
versión impresa ISSN 0327-4411versión On-line ISSN 2362-3675
Resumen
FINUCCI CURI, Pablo. Schnitzler syndrome treated with canakinumab. Rev. argent. reumatolg. [online]. 2019, vol.30, n.3, pp.34-37. ISSN 0327-4411.
Schnitzler syndrome is a rare disorder characterized by chronic urticarial rash and monoclonal gammopathy, accompanied by intermittent fever, arthralgia or arthritis, bone pain and lymphadenopathy, in which interleukin 1 (IL-1) has a preponderant role. The case of a 48-year-old male who meets criteria for Schnitzler syndrome and who after failing too many treatments presents a successful response to canakinumab is presented here.
Palabras clave : Schnitzler syndrome; canakinumab.